45 year old with chronic bilateral hearing loss for cochlear implant assessment
CT axial noncontrast bone windows

CT coronal reconstructions noncontrast bone windows

T2 axials
Findings:
CT: Subtle
demineralization surrounding both the
right and left cochlea, worse on
the right side
MRI: Increased T2 signal surrounding the cochlea bilaterally
DDX:
Cochlear otosclerosis
Diagnosis:
Cochlear otosclerosis
Discussion:
Cochlear otosclerosis is an uncommon cause of mixed and sensorineural
hearing loss. It has a characteristic appearance on CT, producing
a distinctive pericochlear hypodense double ring. However, its
appearance on MRI is not as readily appreciated, producing a
ring of intermediate signal in the pericochlear and perilabyrinthine
regions on T2 and T1 weighted images sometimes with enhancement.
Submitted by Hari Challa, MD, UW Neuroradiology Fellow
Return to UW Neuroradiology Teaching Files